ABSTRACT
Encephalocele is the herniation of the cranial contents through a bone defect in the skull. Nasal encephalocele is the herniation of cranial content in the nasal area. It is a congenital abnormality. It is one of the causes of craniospinal dysraphism, usually present at birth with symptom of obstruction or other complications. It presents as an external swelling on the nose. Clinically, there can be many differential diagnoses. An accurate diagnosis can reduce life threating intracranial complications and permit better management. For proper management, a multidiciplinary approach is needed. Approximately 80% of encephalocele exit the cranial cavity in the region of the occiput. Extraoccipital encephalocoele may protrude through defects in other portions of the cranial vault. We present a case of encephalocele in a 6-month-old girl who presented with a congenital swelling on the left lateral side of the nose with complaints of watering from the eye of same side